TWO CASES OF PANPERITONITIS SECONDARY TO INTESTINAL BEHCET DISEASE
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چکیده
منابع مشابه
Introducing Two Cases of Farber Disease
Lipogranulomatosis or Farber's disease in a rare autosomal recessive disorder characterized by swollen, tender joints, periarticular and subcutaneous nodules, horsncss and progressive aphonia. Hepatosplcnomcgaly and C.N.S. involvements arc also reported in certain patients. The disorder is caused by a deficiency of acid ceramidase which may be best diagnosed by missing ceramidasc activity at a...
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BACKGROUND Behcet's disease (BD) is a chronic immune-mediated, inflammatory disorder which may affect a number of different systems (oral and genital mucosa, eyes, skin, vascular district, joints, gastrointestinal tract and nervous system). Neurological manifestations are present in 5-10%, and gastrointestinal tract involvement in 10-15% of cases. The simultaneous involvement of two systems, ne...
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CONCLUSION Apres avoir discute l'etiologie et la pathogenie de la maladie de Beh<;et, nous avons essaye de traiter trois patients atteints de cette maladie, par Jes immunosuppresseurs. Les resultats ont etc les suivants: I -Dans un cas le resultat est excellent; Ia vision est presque normalisee. 2 -Le deuxieme cas montre une amelioration partielle de la vision depuis 3 ans, sans aucune...
متن کامل[Behcet disease].
Central nervous system involvement in Behçet disease (BD) may be either parenchymal or nonparenchymal. Abnormal cerebrospinal fluid findings and parenchymal involvement are associated with a poorer prognosis. A self-antigenic role for HLA B51 has been postulated in the pathogenesis of BD. The sibling occurrence rate is 3.6%. Familial aggregation may be more pronounced among pediatric cases comp...
متن کاملImmunology of Behcet disease: review article
Behçet's disease (BD), also known as the Silk Road disease, is a multisystemic and rare inflammatory disorder primarily prevalent in populations along the Mediterranean Sea. Today, BD is defined as a crossroad between autoimmune and auto-inflammatory syndromes. Variety of syndromes including mucocutaneous manifestations such as oral and genital ulcers, papulopustular lesions and erythema nodosu...
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ژورنال
عنوان ژورنال: Nihon Rinsho Geka Gakkai Zasshi (Journal of Japan Surgical Association)
سال: 1998
ISSN: 1882-5133,1345-2843
DOI: 10.3919/jjsa.59.2054